Loeys-Dietz Syndrome: Seeing the Whole Vascular Picture

LDS can involve aggressive aneurysms and arterial changes. Longitudinal records help teams coordinate imaging, medications, and surgery decisions.

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Quick Summary

Loeys-Dietz syndrome is a connective tissue condition with a risk of widespread aneurysms and dissections. Centralizing imaging and clinical details helps the care team move fast and in sync.

What is Loeys-Dietz syndrome

LDS is a heritable connective tissue disorder associated with changes in genes along the TGF beta pathway. It can involve arterial tortuosity, aneurysms, and craniofacial features. See the Loeys-Dietz Foundation, NIH GARD, and GeneReviews.

Why a longitudinal view helps

  • Whole-arterial surveillance: track measurements across multiple vascular beds
  • Surgical thresholds and timing: keep prior diameters and Z scores to inform decisions
  • Comorbidities and allergies: LDS can include allergic and inflammatory conditions that matter for care
  • Family genetics and pregnancy plans: organize results and counseling notes for quick reference

How Aether supports LDS care

  • Stores cross-sectional imaging and echo reports with a simple measurement history
  • Consolidates meds, vitals, clinic letters, and procedure notes
  • Secure sharing to vascular surgery, cardiology, genetics, and anesthesia teams

Related reading

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